Saratov JOURNAL of Medical and Scientific Research

Idiopathic syringomyelia with involvement of all segments of spinal cord

Year: 2019, volume 15 Issue: №1 Pages: 180-182
Heading: Neurology Article type: Case report
Authors: Sergeeva А.А., Serebrennikov N.A.
Organization: First City Clinical Hospital n.a. E.E. Volosevich of Arkhangelsk, Northern State Medical University

Syringomyelia is a chronic disease with multiple etiologies characterized by a progressive development of longitudinal cavities within spinal cord, which are filled with cerebrospinal fluid or a liquid of similar composition. Etiologically syringomyelia is most often associated with type 2 Chiari malformation. One of the least common variants is an idiopathic syringomyelia. The article describes a rare clinical case of idiopathic syringomyelia with involvement of all spinal cord segments and the outcomes of its surgical treatment using syringo-subarachnoid shunting techinque.

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