Saratov JOURNAL of Medical and Scientific Research

Clinical case of the Besnier-Boeck-Shaumann syndrome in dermatology practice

Year: 2018, volume 14 Issue: №4 Pages: 755-757
Heading: Dermatovenerology Article type: Case report
Authors: Slesarenko N.A., Morrison A.V., Marchenkna E.M., Moiseev A.A., Roshchepkin V.V.
Organization: Saratov State Medical University

Sarcoidosis (Besnier-Boeck-Schaumann syndrome) is a benign systemic disease, which is based on the defeat of the reticuloendothelial system with the formation of epithelioid cell granulomas without caseosa and perifocal inflammation in the absence of Mycobacterium tuberculosis. It occurs in all countries of the world, but the highest incidence is recorded in Northern Europe and the United States. The incidence ranges from 11 to 35 per 100,000 population. The etiology of the disease is unknown. The pathogenesis is based on delayed hyperergic immune reactions, which lead to the formation of granulomas involving T cells, as well as the release of various chemokines and cytokines, including tumor necrosis factor (TNF-alpha). The aim of the work is to present a clinical case, due to the rarity of dermatosis, as well as the complexity of diagnosis.

Keywords: rare dermatoses

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