Saratov JOURNAL of Medical and Scientific Research

Difficult diagnosis in a dermatologist's practice (description of a clinical case of late cutaneous porphyria)

Year: 2015, volume 11 Issue: №3 Pages: 450-453
Heading: Dermatovenerology Article type: Case report
Authors: Utz S.R., Bakulev A.L., Slesarenko N.A., Eremina M.G., Muratova D.S.
Organization: Saratov State Medical University

The article presents a case report of clinical observations of late cutaneous porphyria in a 50-years old patient. The data of the etiology, pathogenesis and clinical picture are summarized. A differential diagnosis with vulgar disease, acquired epidermolysis bullosa and pseudoporphyria. The results of a successful comprehensive treatment of disease by drugs quinoline series, systemic glucocorticosteroids, phlebotomy.

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